Prenatal diagnosis and fetal therapy adenomatoid malformation type I of five cases of the congenital cystic lung : a report of
نویسندگان
چکیده
We experienced five pregnancy cases with type I congenital cystic adenomatoid malfbrmation (CCAM) of fetuses and summarized here their clinical characteristics, pregnancy outcomes, and feta] therapies. Four of five cases were prenatally diagnosed using magnetic resonance imaging (MRI) as having lung abnormality, and the remaining case was prenatal]y diagnosed as having congenital diaphragmatic herniation (CDH). One fetus underwent the puncture of cysts in the tung, and two fetuses received in utero thoracoshunts between cysts and the amniotic fluid cavity (thoracoamniotic shunt). One pregnancy ended in artificial termination at 17 gestationa} weeks, and 4 pregnancies succeeded in live births. All these 4 infants underwent surgical operations for CCAM, and 1 infant underwent an additional operation for CDH. The MRI examinations were useful to prenatally identify CCAM, and the in utero thoracoamniotic shunt appears to be beneficial in preventing lung hypoplasia in the affected fetuses.
منابع مشابه
Congenital Cystic Adenomatoid Malformation (CCAM) of Lung in an Infant: A Case Report from Jammu & Kashmir, Northern India
Congenital cystic Adenomatoid malformation is a rare developmental abnormality of the lung occuring in 1-4/100000 live births.In most cases the outcome with CCAM in fetus is very good,while in some cases the outcome is very bad and can be life threatning for the fetus.we report here a case of 40 day old female infant who presented with worsening respiratory distress since birth and x ray and CT...
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